Objective: To describe a case of a subcutaneous, extradural, retro sacral, myxopapillary ependymoma which presented as a pilonidal cyst.
Case description: A 6-year old boy presented with a painful intergluteal mass. The histopathologic examination revealed an ependymal neoplasm with conspicuous myxopapillary appearance.
Conclusion: These tumors are extremely unusual in extradural locations, and their biological behavior is more aggressive than those cases of similar histogenesis localized in the conus medullaris-filum terminale region.
